• Media type: E-Article
  • Title: CFTR and lung homeostasis
  • Contributor: Collawn, James F.; Matalon, Sadis
  • Published: American Physiological Society, 2014
  • Published in: American Journal of Physiology-Lung Cellular and Molecular Physiology, 307 (2014) 12, Seite L917-L923
  • Language: English
  • DOI: 10.1152/ajplung.00326.2014
  • ISSN: 1040-0605; 1522-1504
  • Origination:
  • Footnote:
  • Description: CFTR is a cAMP-activated chloride and bicarbonate channel that is critical for lung homeostasis. Decreases in CFTR expression have dire consequences in cystic fibrosis (CF) and have been suggested to be a component of the lung pathology in chronic obstructive pulmonary disease. Decreases or loss of channel function often lead to mucus stasis, chronic bacterial infections, and the accompanying chronic inflammatory responses that promote progressive lung destruction, and, eventually in CF, lung failure. Here we discuss CFTR's functional role airway surface liquid hydration and pH, in regulation of other channels such as the epithelial sodium channel, and in regulating inflammatory responses in the lung.
  • Access State: Open Access