• Medientyp: E-Artikel
  • Titel: Lipid binding promotes the open conformation and tumor-suppressive activity of neurofibromin 2
  • Beteiligte: Chinthalapudi, Krishna; Mandati, Vinay; Zheng, Jie; Sharff, Andrew J.; Bricogne, Gerard; Griffin, Patrick R.; Kissil, Joseph; Izard, Tina
  • Erschienen: Springer Science and Business Media LLC, 2018
  • Erschienen in: Nature Communications, 9 (2018) 1
  • Sprache: Englisch
  • DOI: 10.1038/s41467-018-03648-4
  • ISSN: 2041-1723
  • Entstehung:
  • Anmerkungen:
  • Beschreibung: AbstractNeurofibromatosis type 2 (NF2) is a tumor-forming disease of the nervous system caused by deletion or by loss-of-function mutations in NF2, encoding the tumor suppressing protein neurofibromin 2 (also known as schwannomin or merlin). Neurofibromin 2 is a member of the ezrin, radixin, moesin (ERM) family of proteins regulating the cytoskeleton and cell signaling. The correlation of the tumor-suppressive function and conformation (open or closed) of neurofibromin 2 has been subject to much speculation, often based on extrapolation from other ERM proteins, and controversy. Here we show that lipid binding results in the open conformation of neurofibromin 2 and that lipid binding is necessary for inhibiting cell proliferation. Collectively, our results provide a mechanism in which the open conformation is unambiguously correlated with lipid binding and localization to the membrane, which are critical for the tumor-suppressive function of neurofibromin 2, thus finally reconciling the long-standing conformation and function debate.
  • Zugangsstatus: Freier Zugang