• Medientyp: E-Artikel
  • Titel: Cerebrospinal Fluid Findings in Neurological Diseases Associated with Sjögren's Syndrome
  • Beteiligte: Pars, Kaweh; Pul, Refik; Schwenkenbecher, Philipp; Sühs, Kurt-Wolfram; Wurster, Ulrich; Witte, Torsten; Bronzlik, Paul; Stangel, Martin; Skripuletz, Thomas
  • Erschienen: S. Karger AG, 2017
  • Erschienen in: European Neurology, 77 (2017) 1-2, Seite 91-102
  • Sprache: Englisch
  • DOI: 10.1159/000454765
  • ISSN: 0014-3022; 1421-9913
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  • Beschreibung: <b><i>Background:</i></b> Sjögren's syndrome is a chronic autoimmune-mediated disease that can cause a variety of neurological manifestations. <b><i>Methods:</i></b> This study investigated characteristics of clinical and cerebrospinal fluid (CSF) features in patients with neurological diseases associated with Sjögren's syndrome. Eighty-two patients were examined separately according to the presence of Sjögren's syndrome alone or in combination with other autoimmune diseases. <b><i>Results:</i></b> In the 47 patients with primary Sjögren's syndrome, peripheral neuropathy (57%) was found most frequently, followed by the involvement of the central nervous system (CNS; 17%), cranial neuropathy (15%), and myalgia (11%). These patients did not display consistent signs of inflammation in the CSF. Slight pleocytosis of 8-107 cells/µL was found in patients with peripheral neuropathy (9%), cranial neuropathy (20%), and CNS involvement (25%). Oligoclonal bands indicating intrathecal IgG synthesis occurred in 26% of patients with peripheral neuropathy, 20% of patients with cranial neuropathy, and 25% of patients with CNS involvement. <b><i>Conclusions:</i></b> In patients with Sjögren's syndrome and neurological manifestations, inflammatory CSF changes were rarely found and did not show a characteristic pattern irrespective of peripheral or central genesis of neurological deficits. Analysis of the CSF presents therefore an important diagnostic procedure to exclude other autoimmune and infectious diseases.